Abstract: Primordial uterus, also known as trace uterus, is a special congenital uterine abnormality. Primordial uterus is extremely small, only 1-3 cm in length. It is a rare disease, and its etiology is still unclear. By reviewing the clinical data of a patient with bilateral primordial uterus complicated with ovarian mucinous cystadenomatosis in Binzhou Medical University Hospital and reviewing relevant literatures, this paper aims to understand the research progress of the disease and provides ideas for physicians to diagnose and treat such patients clinically.

Key words: Primordial uterus, Ovarian tumor, Mucinous cystadenoma, Mullerian duct, Gene mutation

摘要： 始基子宫又称痕迹子宫，是一种特殊的先天性子宫发育异常，始基子宫极小，长径为1～3 cm，属罕见病，其病因尚不明确。本文通过回顾滨州医学院附属医院收治的1例双侧始基子宫合并卵巢黏液性囊腺瘤病患者的临床资料，并进行相关文献复习，旨在了解疾病相关研究进展，为医师在临床上诊治此类患者提供思路。

关键词: 始基子宫, 卵巢肿瘤, 黏液性囊腺瘤, 苗勒管, 基因突变