Abstract:

The overall nursing experience of a child with X-linked adrenoleukodystrophy who received allogeneic hematopoietic stem cell transplantation was summarized. The main nursing measures were as below. ⑴Preparation before transplantation: early identification of changes in the conditions and comprehensive nursing evaluation; strengthening education on disease and transplant related knowledge, providing personalized psychological care interventions, and ensuring the patients' and their families' psychological health. ⑵Nursing during transplantation: strict medication management during the pre-treatment period of transplantation to ensure medication safety; strictly implementing sterile procedures and safely administering hematopoietic stem cells. ⑶Post transplantation management: close monitoring and early detection and management of transplant related complications; strictly implementing infection prevention and control measures; providing targeted health education and continuous care. After 68 days' careful treatment and care, the patient was successfully implanted and discharged with stable conditions.

Key words:

X-linked adrenoleukodystrophy, Hematopoietic stem cell transplantation, Pediatric nursing

摘要：

总结1例肾上腺脑白质营养不良患儿接受异基因造血干细胞移植治疗的整体护理经验。其主要护理措施如下。⑴移植前准备：早期识别病情变化，实施整体性护理评估；加强疾病及移植相关知识宣教，给予个性化心理护理干预，保障患儿及家属心理健康。⑵移植期间护理：移植预处理期严格用药管理，确保用药安全；严格执行无菌操作，安全输注造血干细胞。⑶移植后管理：密切监测，早期发现并处理移植相关并发症；严格执行感染预防及控制措施；给予针对性健康宣教及延续性护理。经过68 d精心治疗和护理，患儿成功植入造血干细胞，病情稳定出院。

关键词:

肾上腺脑白质营养不良, 造血干细胞移植, 儿科护理