透明细胞乳头状肾细胞肿瘤1例并文献复习

doi:10.3760/cma.j.issn.1007-1245.2024.10.029

摘要/Abstract

摘要：

透明细胞乳头状肾细胞肿瘤（CCPRCT）是一种具有低度恶性潜能的肾脏肿瘤。本文回顾性分析暨南大学附属第一医院2021年8月收治的1例术后病理诊断为CCPRCT的中年男性患者临床资料及影像学资料并复习相关文献。超声表现：左肾上极低回声结节，大小3.8 cm×2.6 cm×3.0 cm，边界尚清，内见小片状无回声区，部分突向肾外。彩色多普勒血流显像：结节周围见少许血流信号。超声造影：快进，慢退，不均匀高增强。磁共振成像示：左肾上极见一分叶状肿块影，大小4.0 mm×2.9 mm×2.7 mm，边界清，边缘光滑，T1加权成像以低信号为主，T2加权成像呈等-高信号，内见蜂房状高信号灶及T2加权成像低信号成分。增强扫描见实性成分动脉期明显强化，平衡期强化稍减退，延迟期强化稍低于正常肾实质，病灶内条形T2低信号成分延迟强化，磁共振弥散加权成像上病灶呈不均匀高信号。磁共振成像提示：左肾上极占位性病变，考虑肾癌可能性大。

关键词:

乳头状肾细胞癌, 透明细胞乳头状肾细胞肿瘤, 超声检查, 诊断显像, 文献复习

Abstract:

Clear cell papillary renal cell tumor (CCPRCT) is a renal tumor with low malignant potential. This article retrospectively analyzed the clinical and radiographic data of middle-aged male patient with CCPRCT in the First Affiliated Hospital of Jinan University in August 2021 and reviewed the relevant literature.. Ultrasound showed a hypoechoic nodule at the upper pole of the left kidney, measuring about 3.8 cm × 2.6 cm × 3.0 cm, with clear borders, and a small patchy echogenic area within the nodule, part of the nodule protruding outside the kidney. Color Doppler flow imaging (CDFI) showed a little blood flow signal around the nodule. Contrast-enhanced ultrasound (CEUS) showed fast-forward and slow-retreat, inhomogeneous hyperenhancement. Magnetic resonance imaging (MRI) showed a lobulated mass at the upper pole of the left kidney, measuring about 4.0 mm × 2.9 mm × 2.7 mm, with clear borders and smooth edges, predominantly hyposignal on T1WI and equal-high signal on T2WI, with a honeycomb-shaped hypersignal foci and a low-signal component on T2WI within the mass. Enhancement scan showed obvious enhancement of the solid component in the arterial phase, slightly reduced enhancement in the equilibrium phase, and delayed enhancement slightly lower than normal renal parenchyma; the T2 low-signal strips within the mass were delayed enhancement, and the mass was unevenly high-signal on diffusion weighted imaging (DWI). MRI showed occupying lesions in the upper pole of the left kidney, which were considered to be a high probability of renal cancer.

Key words:

Papillary , renal , cell , carcinoma, Clear , cell , papillary , renal , cell , tumor, Ultrasonic , diagnosis, Diagnostic , imaging, Literature , review

黄钰华梁银莹黄君.

透明细胞乳头状肾细胞肿瘤1例并文献复习 [J]. 国际医药卫生导报, 2024, 30(10): 1726-1729.

Huang Yuhua, Liang Yinying, Huang Jun.

A case of clear cell papillary renal cell tumor and literature analysis [J]. International Medicine and Health Guidance News, 2024, 30(10): 1726-1729.

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