Abstract:

Hypertrophic pachymeningitis (HP) is a chronic fibrous inflammatory disease of the spinal dura, and is rare in clinic. It can be divided into hypertrophic cranial pachymeningitis (HCP) and hypertrophic spinal pachymeningitis (HSP), which can exist at the same time. It can be divided into secondary and idiopathic, which may be related to immune factors. The treatment methods include glucocorticoids and other immunosuppression and surgery. Pathology is the gold standard for diagnosis, and magnetic resonance imaging (MRI) enhancement may assist in diagnosis. A case of idiopathic hypertrophic cranial and spinal pachymeningitis in Weihai Central Hospital is reported now.

Key words:

Idiopathic hypertrophic cranial and spinal pachymeningitis, Magnetic resonance imaging, Immunotherapy

摘要：

肥厚性硬膜炎（hypertrophic pachymeningitis，HP）是一种硬脊膜慢性纤维化炎性病变，该病临床少见，分为肥厚性硬脑膜炎（hypertrophic cranial pachymeningitis，HCP）、肥厚性硬脊膜炎（hypertrophic spinal pachymeningitis，HSP），两者可同时存在。分为继发性和特发性，很可能与免疫因素相关，治疗方法包括糖皮质激素等免疫抑制和手术。病理是诊断金标准，核磁增强表现可协助诊断。现报道威海市中心医院1例特发性肥厚性硬脑脊膜炎。

关键词:

特发性肥厚性硬脑脊膜炎, 磁共振成像, 免疫治疗