Ultrasonic diagnosis of dermatofibrosarcoma protuberans: one case report

doi:10.3760/cma.j.issn.1007-1245.2022.04.028

Abstract

Abstract: Dermatofibrosarcoma protuberans (DFSP) is a rare sarcoma in the clinical practice and is easy to be misdiagnosed as other common benign tumors of the skin, so it is necessary to strengthen the understanding on this disease for sonologists to provide important values for clinical preoperative diagnosis and treatment. To investigate the ultrasound features and differential diagnosis of DFSP and improve the preoperative diagnostic accuracy, the clinical data and ultrasound images of a patient with DFSP confirmed by operation and pathology received by The First Affiliated Hospital of Jinan University in July 2019 were retrospectively analyzed. Ultrasound findings showed that a mixed echo nodule was observed in the skin layer of the right breast, ranging about 12 mm×24 mm, with a clear boundary, irregular shape, heterogeneous echo, and strip-like hyper echo. Color Doppler flow imaging (CDFI) showed increased blood flow signals in the nodule.

Key words: Dermatofibrosarcoma protuberans, Ultrasonography, Molybdenum target

摘要： 隆突性皮肤纤维肉瘤（dermatofibrosarcoma protuberans，DFSP）临床上较罕见，容易误诊为皮肤其他常见的良性肿瘤而做常规切除，应加强超声医生对此病的认识，为临床的术前诊断和治疗提供重要价值。为探讨DFSP的超声表现及鉴别要点、提高术前诊断、降低复发风险，现回顾性分析于2019年7月收入暨南大学附属第一医院的经手术病理证实的1例DFSP患者的临床资料及超声表现。超声表现：右侧胸壁处皮肤层见混合回声结节，大小约12 mm×24 mm，边界尚清，形态不规则，回声欠均匀，内见条索状强回声。彩色多普勒血流显像（CDFI）：结节内见丰富的血流信号。

关键词: 隆突性皮肤纤维肉瘤, 超声, 钼靶

Zhang Lisu, Fang Haiyan, Liang Yinying, Huang Jun. Ultrasonic diagnosis of dermatofibrosarcoma protuberans: one case report[J]. International Medicine and Health Guidance News, 2022, 28(4): 556-558.

张莉苏, 方海燕, 梁银莹, 黄君. 超声诊断隆突性皮肤纤维肉瘤1例[J]. 国际医药卫生导报, 2022, 28(4): 556-558.

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